Online first · May 28, 2026
A Single-Center Clinical Analysis of 121 Pediatric Cases with Pulmonary Atresia and Ventricular Septal Defect Undergoing the Pulmonary Artery Flow Study
Fan Cao, Wenhua Liu, Rongjun Zou, Lijuan Li, Na Zhou, Chengbin Zhou, Li Ma
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Background: This study analyzed the utility of the pulmonary artery flow study (PAFS) in prognostic assessment for children with pulmonary atresia and ventricular septal defect (PA/VSD).Methods: We reviewed 121 patients with type B or C pulmonary atresia and …
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Online first · May 28, 2026
Long-term Outcome of Rheumatic Mitral Valve Surgery in Children From Low- and Middle-Income African Nations
François Lacour-Gayet, Emré Belli, Christophe Baufreton, Maguette Ba, Régine Roussin, Francine Leca
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Background: There is limited information on rheumatic mitral valve surgery for children living in low- and middle-income African countries.Patients and methodsFrom 1/1/1998 to 1/1/2024, a total of 276 children <18 years of age, coming from Africa, underwent …
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Online first · June 11, 2026
Anomalous Aortic Origin of the Right Coronary Artery in Adults: Surgical Reimplantation With Intermediate-Term Results
Dina Sabha, Mohammad Alomari, Laith Hyasat, Saif Yamin, Rana Alkirmeen, Ayman Hammoudeh, Pankaj Garg, Bahi Hyasat
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Background: Anomalous aortic origin of the right coronary artery (AAORCA) with an intramural course is a rare but potentially life-threatening anomaly due to its association with exertional ischemia and sudden cardiac death. Surgical correction aims to …
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Online first · June 17, 2026
Substantial Operative and Nonoperative Mortality Persists in Neonatal Ebstein Anomaly: A 20-Year Multi-Institutional Analysis
Darren Turner, Amir Mehdizadeh-Shrifi, Muhammad Faateh, Hosam Ahmed, Michael A. Carlisle, David Lehenbauer, Marco Ricci, Awais Ashfaq, David L. S. Morales12518Cincinnati Children’s Hospital Medical Center, Cincinnati, OH, USA
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Background: We sought to characterize the epidemiology, treatment patterns, and outcomes of neonatal Ebstein anomaly using a national database.Methods: In this descriptive analysis, the pediatric health information system (PHIS) database was queried for the …
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Online first · June 25, 2026
Inhaled Nitric Oxide via High-Flow Nasal Cannula in Postrepair Congenital Heart Disease Patients With Pulmonary Arterial Hypertension Following Extubation: A Cohort Study With Propensity Score Matching
Xiaofeng Wang, Qinnan Chen, Shilin Wang, Zhiyuan Zhu, Hong Gu, Xu Wang
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Objective: :For pediatric patients with congenital heart disease (CHD) and pulmonary arterial hypertension (PAH), corrective repair carries a substantial risk of inducing pulmonary hypertensive crisis (PHC). The conventional clinical strategy involves …
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Online first · June 30, 2026
Integration of the Korean and World Databases for Pediatric and Congenital Heart Surgery: A Model for Global Registry Collaboration
James D. St. Louis, Brian P. Bateson, Taylor Broser, Chae Lin Jeong, Rama Rudraraju, John Pennigton, Sivakumar Sivalingam, Ignacio Lugones, Jeffery P. Jacobs, Christo Tchervenkov, Richard Jonas, James K. Kirklin, Cheul Lee
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Background: :Establishing the Korean Pediatric and Congenital Heart Surgery Database (KPCHSD) and linking it to the World Database for Pediatric and Congenital Heart Surgery (WDPCHS) is an important step toward creating a global network for quality care. …
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Online first · June 25, 2026
Mortality and Risk Factors in Pediatric Cardiac Surgery for Congenital Heart Disease in Mexico
Yoana Leyva-López, José L. Cerano-Fuentes, Juan Calderón-Colmenero, Jorge L. Cervantes-Salazar
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Objective: :To describe surgical outcomes, in-hospital mortality, and variables associated with mortality in pediatric patients with congenital heart disease (CHD) at a national referral center in México over 14 years.Methodology:Retrospective cross-…
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Online first · June 29, 2026
Prostaglandin Administration and Outcomes in Children on Extracorporeal Membrane Oxygenation
Weidi Xiao, Nedaa Aldairi, Brian S. Marcus, Matthew Weiss, Allison S. Cowl, Marissa Moncata, Akash Deep, Oliver Karam
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Objective: sExtracorporeal Membrane Oxygenation (ECMO) is associated with high risks of bleeding and clotting. While traditional anticoagulants like heparin and bivalirudin target the coagulation cascade, prostaglandins including PGE1and PGI2may offer …
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Online first · July 3, 2026
Mechanical Mitral Valve Replacement in Patients Under 18 Years of Age
Akiko Yamagata, Takeshi Shinkawa, Akihisa Furuta, Hisashi Yoshida, Satoshi Saito, Hiroshi NiinamiDepartment of Cardiovascular Surgery, 13131Heart Institution of Japan, Tokyo Women’s Medical University, Tokyo, Japan
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Background: Pediatric mechanical mitral valve replacement (mMVR) is a high-risk procedure associated with long-term complications and lifelong anticoagulation. This study aimed to evaluate long-term outcomes of mMVR in patients under 18 years of age and to …
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Online first · May 15, 2026
The Aortic Uncrossing Procedure in a Two-Year Old Child with a Circumflex Left Aortic Arch and a Right Sided Arterial Duct: Technical Details with 1-Year Follow-Up
Mani Ram Krishna, Usha Nandhini Sennaiyan, Naveen Srinivasan, Vijaykumar Raju
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Circumflex aortic arch is a rare vascular ring, with the circumflex right aortic arch much more common than a left aortic arch. The aortic uncrossing procedure has become the surgical intervention of choice for this anomaly. In younger children, some …
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Online first · May 28, 2026
A Rare Case of Ischemia Associated with Anomalous Cardiac Venous Drainage in an Infant
Paulina Kopacz, Luzia Zalewska, Grzegorz Gęca, Krzysztof Kocot, Richard D. Mainwaring, Grzegorz Zalewski
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Anomalous cardiac venous drainage is a rarely reported condition typically associated with atresia of the coronary sinus ostium. We present a very unusual case of a newborn with dual drainage of the cardiac veins to both the coronary sinus and to a …
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Online first · May 28, 2026
Patent Ductus Arteriosus and Left Mainstem Bronchus Compression in a Term Infant: Broad Differential, Novel Diagnostics, and Surgical Resolution
Christhian A. Cano-Guerra, Philip T. Levy, Peter Chiu, Jessica E. Shui
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
The differential diagnosis of respiratory distress in term neonates is broad and includes infectious, cardiac, parenchymal, airway, metabolic, and genetic etiologies. We present the case of a full-term, 10-day-old infant with tachypnea, feeding …
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Online first · May 28, 2026
Coronary-Sparing Resection of a Pediatric Left Ventricular Fibroma Involving the Left Circumflex Artery: Six-Year Follow-Up
Manuela Silva Lopes, Maria Emanuel Amaral, Andreia Francisco, Maria Conceição Sanches, Rebecca S. Beroukhim, Helena Andrade, António Pires
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Left ventricular (LV) fibromas in children can pose major surgical challenges when epicardial coronary arteries are involved. We report the case of a 3-month-old female diagnosed with a large intramyocardial LV fibroma causing mitral valve compression and …
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Online first · May 29, 2026
Giant Left Atrial Appendage Aneurysm in an Adolescent: Resection With Patent Foramen Ovale Closure
Maria Mihailescu, Collin Kramer, Adam B. Christopher, Sameh S. Tadros, Luciana Da Fonseca Da Silva, Richard Tang
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
A 14-year-old female was incidentally found to have a giant left atrial appendage aneurysm (LAAA) and patent foramen ovale (PFO) on computed tomography, confirmed by transthoracic echocardiography. Given the inherent risk of arrhythmia and thromboembolic …
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Online first · May 29, 2026
Innominate Artery Compression Syndrome Following Endovascular Stenting of Tracheoinnominate Artery Fistula
Kolapo Dairo, Monirah Albathi, Jonathan Grischkan, Sergio A. Carrillo
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Tracheoinnominate artery fistula (TIF) is a life-threatening complication associated with tracheostomy placement. It is characterized by the development of a connection from the tracheal lumen to the innominate artery. We describe the multidisciplinary …
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Online first · June 30, 2026
Acute Severe Left Atrioventricular Valve Regurgitation Secondary to Spontaneous Rupture of Chordae Tendinae in a Patient with Down Syndrome
Rukmini Komarlu, Rida Shahid, John Costello, Munir Ahmad, Hani K Najm
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
We present a unique case of spontaneous chordal rupture in a young infant with Down syndrome and unrepaired transitional atrioventricular septal defect. This resulted in abrupt onset of severe left atrioventricular valve regurgitation, cardiogenic shock, …
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Online first · May 19, 2026
Valve-Sparing Root Replacement Following Congenital Heart Disease Repair: Lesion-Specific Technical Considerations
Yuchen Cao, Masaaki Koide, Yoshifumi Kunii, Masafumi Yashima, Daisuke Takahashi, Takuya Maeda, Kumiko Sone, Satoru Nishiyama1Department of Cardiovascular Surgery, Seirei Hamamatsu General Hospital, Hamamatsu, Japan
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Valve-sparing root replacement (VSRR) is increasingly used for aortic root dilatation following congenital heart disease repair; however, technical differences between lesions are rarely described. Here, we present three adult cases of VSRR following …
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Online first · June 3, 2026
Implantability of the Konect Resilia Aortic Valved Conduit in the Pulmonary Position
Jerome Soquet, Christina Shoba Rajamanickam, Ashutosh Hardikar1Cardiothoracic Surgery, 1062Royal Adelaide Hospital, Adelaide, SA, Australia
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
The Konect Resilia valved conduit (Edwards Lifesciences) was designed for aortic valve and root replacement. This article aims to describe its use in the pulmonary position (off-label). This graft is particularly convenient when the pulmonary bifurcation …
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Online first · May 20, 2026
Quality Improvement in Congenital Heart Surgery Requires Data: Is This Asking too Much in Low- and Middle-Income Countries?
Debasis Das, Shubhadeep Das, Bistra Zheleva, Sivakumar Sivalingam, Ulisses Alexandre Croti, Bruna Cury, Krishna Subramony Iyer
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Quality improvement (QI) in congenital heart surgery depends mainly on the availability of reliable, organized, and usable data. While high-income countries benefit from mature national registries and well-established benchmarking systems, low- and middle-…
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Online first · June 11, 2026
Fontan Failure in Adult Patients: From Physiology to Solutions
Egor A. Karev, Oksana F. Stovpyuk, Daria V. Alekseeva, Diana S. Malishevskaya, Lev M. Malishevsky, Anton A. Avramenko
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
The adult population with congenital heart defects of varying complexity is growing rapidly. This includes a significant number of patients over the age of 18 who underwent surgery in early childhood to correct conotruncal anomalies and septal defects. …
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Online first · June 11, 2026
Prostaglandin E1 Following Balloon Atrial Septostomy in Dextro-Transposition of the Great Arteries: Reevaluating Dependence, Timing, and Physiology-Guided Management
Joram Lawrence Nyandat, Jacqueline Chepng’eno Ng’eny
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Dextro-transposition of the great arteries is a critical cyanotic congenital heart defect in which neonatal survival depends on effective intercirculatory mixing. Balloon atrial septostomy (BAS) improves atrial-level mixing; however, many infants remain …
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Online first · May 30, 2026
Surgical Approaches to Coronary Arteries Crossing the Subpulmonary Infundibulum in the Setting of Tetralogy of Fallot
Ujjwal Kumar Chowdhury, Robert H. Anderson, Niraj N. Pandey, Niwin George, Saurabh Kumar Gupta, Maroof A. Khan, Chaitanya Chittimuri, Priya Dubey
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Background: Multiple techniques have been described to surgically address the presence of an anomalous coronary artery crossing the subpulmonary infundibulum in patients with tetralogy of Fallot, with perioperative mortality and ventricular dysfunction both …
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Online first · June 11, 2026
Objective Evaluation of Three-Dimensional Models for Training Congenital Cardiac Surgeons: A Systematic Review
Jeevan Francis, Sara Brophy, Alan George, Nabil Hussein
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Objective: s:This systematic review aimed to evaluate the types, validity, and outcomes of objective assessment tools used to measure surgeon performance during congenital cardiac surgical training using three-dimensional (3D) models.Methods: :A systematic …
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Online first · June 11, 2026
Perioperative Normoxia Versus Hyperoxia in Cyanotic Congenital Heart Surgery: A Systematic Review and Meta-Analysis of Randomized Controlled Trials
Leonardo Braga Gonçalves, Lucas Monteiro Delgado, Rachid Eduardo Noleto da Nobrega Oliveira, Erlon de Ávila Carvalho, Madeline Loftin, Davi Freitas Tenório
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
Background: Optimal oxygenation strategies during cardiopulmonary bypass (CPB) in children with cyanotic congenital heart disease remain controversial. Although hyperoxia has traditionally been used to compensate for chronic hypoxemia, concerns exist …
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Online first · June 25, 2026
Impact of Fenestration on Survival and Morbidity Following Fontan Surgery: A Time-to-Event Meta-Analysis of Reconstructed Kaplan–Meier Data
Rohit Ganduboina, Jef Van den Eynde, Xander Jacquemyn, Omar Abdel Kerim, Sandeep Sainathan
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
IntroductionThe Fontan procedure revolutionized single-ventricle palliation by enabling passive pulmonary blood flow. Fenestration, an atrial-level shunt, reduces early postoperative complications by decompressing the circuit but causes systemic …
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Online first · May 28, 2026
Playing With the Band
Michael C. Mongé1Division of Cardiovascular Surgery, 711318Ann & Robert H. Lurie Children’s Hospital of Chicago, Chicago, IL, USA
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
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Online first · May 22, 2026
Clarifications on the Stanford Intraoperative Flow Study
Richard D. Mainwaring1Stanford University School of Medicine, Division of Pediatric Cardiac Surgery, 6429Lucile Packard Children’s Hospital Stanford, Stanford, CA, USA
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
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Online first · July 3, 2026
Pioneering Cardiac Surgical Outcomes Research in the Brazilian Amazon: Data Challenges, Methodological Choices, and the Value of First Regional Evidence
Luciane Alves da Rocha Amorim, Edward Araujo Júnior
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
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Online first · July 3, 2026
In-Hospital Mortality in Children Undergoing Congenital Heart Surgery in North Brazil: Methodological Considerations on RACHS-1 Interpretation
Marcos Aurelio Barboza de Oliveira, Vinicius Nina, Pedro Rafael Salerno, Valdester Cavalcante Pinto Junior
World Journal for Pediatric and Congenital Heart Surgery, Ahead of Print.
