PA-VSD Without MAPCA(s): Review of Long-Term Outcomes and Reinterventions
Published: July 23, 2024.
Volume 16, Number 2
Pages 232-236
Contributors
Elizabeth H. Stephens, Joseph A. Dearani, William R. Miranda, Jason H. Anderson
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 232-236, March 2025.
BackgroundPulmonary atresia with ventricular septal defect without major aortopulmonary collateral arteries (MAPCAs) is an uncommon form of congenital heart disease. As more patients with congenital heart disease live to adulthood, the objective of this …
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Pulmonary Atresia and Ventricular Septal Defect Without Major Aortopulmonary Collateral Arteries: Diagnostic Evaluation and the Role of Ductal Stenting
Published: September 05, 2024.
Volume 16, Number 2
Pages 197-202
Contributors
Jeannette R. Wong-Siegel, Christopher J. Petit, Andrew C. Glatz
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 197-202, March 2025.
Patients with pulmonary atresia (PA) and a ventricular septal defect (VSD), similar to those with tetralogy of Fallot and PA without major aortopulmonary collateral arteries, lack antegrade pulmonary blood flow, and thus require a neonatal intervention …
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Mid-Term Results of Pulmonary Valve-Sparing Repair for Tetralogy of Fallot With Pulmonary Stenosis
Published: November 07, 2024.
Volume 16, Number 2
Pages 237-245
Contributors
Vijayakumar Raju, Naveen Srinivasan, Divya Kadavanoor, Rajalakshmi Moorthy, Kousik Jothinath, Sreja Gangadharan, Aparna Vijayaraghavan, Kalyanasundaram Muthuswarmy, Mani Ram Krishna, Pavithra Ramanath
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 237-245, March 2025.
ObjectiveThe transannular patch remains the most common procedure performed for patients with Tetralogy of Fallot (TOF) with pulmonary stenosis. Pulmonary regurgitation has a negative impact on early and late outcomes. To address this issue pulmonary …
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Management of Tricuspid Atresia With Normally Related Great Arteries and Left-Sided Obstruction
Published: November 19, 2024.
Volume 16, Number 2
Pages 254-261
Contributors
Andres M. Palacio, William G. Williams, David J. Barron, Madison B. Argo, Anusha Jegatheeswaran, Marshall L. Jacobs, Igor Bondarenko, Karl F. Welke, James K. Kirklin, Tara Karamlou, Bahaaldin Alsoufi, Brian W. McCrindle,
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 254-261, March 2025.
BackgroundTricuspid atresia (TA) is the second most common form of functionally univentricular heart. For patients with TA and normally related great arteries (Type I), left ventricular outflow tract obstruction (LVOTO) is rare.MethodsFrom the Congenital …
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Pulmonary Atresia With Ventricular Septal Defect Without Major Aorto-Pulmonary Collateral Arteries: Echocardiography and the Role of Computed Tomography and Magnetic Resonance Imaging
Published: January 13, 2025.
Volume 16, Number 2
Pages 183-190
Contributors
Sarah Chambers Gurson3313Department of Pediatrics, Inova Health System, Falls Church, VA, USA
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 183-190, March 2025.
Pulmonary atresia with ventricular septal defect (PA-VSD) is usually diagnosed by transthoracic or fetal echocardiography, with the prenatal diagnosis being feasible and accurate if fetal cardiology services are available. The limitations of transthoracic …
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Legacy and Leadership: Celebrating the Contributions of Six Visionary Presidents of the World Society for Pediatric and Congenital Heart Surgery
Published: January 23, 2025.
Volume 16, Number 2
Pages 159-170
Contributors
James Kirklin1Kirklin Solutions Inc, Birmingham, AL, USA
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 159-170, March 2025.
Leadership in pediatric and congenital heart surgery requires a distinctive blend of clinical mastery, scientific innovation, and an unwavering commitment to education and mentorship. The individuals who rise to the top of this demanding field exhibit not …
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Peritoneal Dialysis Catheter Placement on the Right Side of the Falciform Ligament to Prevent Obstruction by the Omentum
Published: December 20, 2024.
Volume 16, Number 2
Pages 273-275
Contributors
F. Doig, H. Kheslat, Y. d’Udekem, S. P. Namachivayam, A. J. Iyengar
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 273-275, March 2025.
We describe a simple and reproducible technique for neonatal peritoneal dialysis catheter insertion following cardiac surgery which prevents the catheter from becoming blocked by the omentum.
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Pulmonary Atresia and Ventricular Septal Defect: Definitions, Nomenclature, and Classification
Published: February 06, 2025.
Volume 16, Number 2
Pages 173-176
Contributors
Christo I. Tchervenkov, Richard Tang, Giles J. Peek, Mark S. Bleiweis, Jeffrey P. Jacobs
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 173-176, March 2025.
This manuscript will provide information about pulmonary atresia + ventricular septal defect, including definitions, nomenclature, and classification, based on the 2021International Paediatric and Congenital Cardiac Code(IPCCC) and theEleventh Revision …
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Rehabilitation Strategy Should Not Be a Pretext for Suboptimal Repair for Pulmonary Atresia, Ventricular Septal Defect, and Major Aortopulmonary Collateral Arteries
Published: February 21, 2025.
Volume 16, Number 2
Pages 227-231
Contributors
Manan H. Desai, Aybala Tongut, Yves d’Udekem8404Children’s National Health System, Washington, DC, USA
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 227-231, March 2025.
Pulmonary atresia, ventricular septal defect, and major aortopulmonary collaterals are a challenging congenital anomaly to manage surgically with different centers and strategies producing wide-ranging outcomes. Over the past few decades despite diverging …
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Pulmonary Atresia, Ventricular Septal Defect, and Major Aortopulmonary Collateral Arteries: The Natural History and Late Presentation
Published: February 05, 2025.
Volume 16, Number 2
Pages 203-207
Contributors
Darshan Reddy, Robert Kleinloog, Robin Kinsley
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 203-207, March 2025.
Pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries represents a heterogenous and complex congenital heart defect. Treatment pathways vary widely depending on center expertise. The recommended approach in infancy …
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Infracardiac Total Anomalous Pulmonary Venous Connection With Meandering Intrapulmonary Vertical Vein Masquerading as a Scimitar Vein
Published: February 21, 2025.
Volume 16, Number 2
Pages 276-278
Contributors
Damandeep Singh, Niraj Nirmal Pandey, Aprateem Mukherjee, Ankur Handa, Lamk Kadiyani, Vatsal Vora, Pradeep Ramakrishnan, Sanjeev Kumar
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 276-278, March 2025.
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Risk Factors and Outcomes of Perioperative Extracorporeal Membrane Oxygenation in Neonates and Infants Undergoing Truncus Arteriosus Repair
Published: October 25, 2024.
Volume 16, Number 2
Pages 246-253
Contributors
Lily Suh, Jason R. Buckley, Jessica E. Hook, Dennis R. Delany, Minoo N. Kavarana, Shahryar M. Chowdhury, Laura E. Hollinger, John M. Costello
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 246-253, March 2025.
Background:Despite surgical advances, neonatal truncus arteriosus repair remains high risk and approximately 10% of patients receive perioperative extracorporeal membrane oxygenation (ECMO). We aimed to assess factors and outcomes associated with the use …
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Tetralogy of Fallot With Pulmonary Atresia and Major Aortopulmonary Collateral Arteries: Diagnostic Modalities—The Role of Computed Tomography, Cardiac Magnetic Resonance Imaging, and Three-Dimensional Modeling
Published: February 21, 2025.
Volume 16, Number 2
Pages 191-196
Contributors
Reena M. Ghosh, Mara Thompson11862Department of Cardiac Surgery, Boston Children’s Hospital, Boston, MA, USA
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 191-196, March 2025.
Cross-sectional imaging modalities facilitate thenoninvasiveacquisition of anatomic and hemodynamic data in patients with congenital heart disease. This is critical in patients with tetralogy of Fallot with pulmonary atresia and major aortopulmonary …
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Early Outcomes for Management of Atrioventricular Septal Defect—Tetralogy of Fallot in the Last Decade: A Congenital Heart Surgeons’ Society Study
Published: November 21, 2024.
Volume 16, Number 2
Pages 262-272
Contributors
Connor P. Callahan, Madison B. Argo, Brian W. McCrindle, David J. Barron, Anusha Jegatheeswaran, Osami Honjo, Anastasios C. Polimenakos, Joseph W. Turek, Robert J. Dabal, James K. Kirklin, William M. DeCampli, Pirooz Eghtesady, David M. Overman,
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 262-272, March 2025.
BackgroundWe sought to determine the management and early outcomes of complete atrioventricular septal defect—tetralogy of Fallot (AVSD-TOF) for a contemporary multicenter cohort.MethodsOf 739 participants in the Congenital Heart Surgeons’ Society AVSD …
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Single-Stage Midline Unifocalization Is Associated With Excellent Outcomes in Infants of All Ages
Published: January 29, 2025.
Volume 16, Number 2
Pages 218-226
Contributors
Elisabeth Martin, Michael Ma, Yulin Zhang, Ritu Asija, Jennifer Shek, Chandra Ramamoorthy, Frank L. Hanley, Doff B. McElhinney
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 218-226, March 2025.
ObjectiveTetralogy of Fallot, pulmonary atresia, and major aortopulmonary collateral arteries are a complex congenital heart defect. For years, our program has recommended early single-stage midline unifocalization at three to six months of age. However, …
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Intraconal Left Main Coronary Artery Originating From the Left Sinus of Valsalva
Published: November 11, 2024.
Volume 16, Number 2
Pages 279-281
Contributors
Arvind Bishnoi, Richard D. Mainwaring, Anna Seehofnerova, Frank L. Hanley
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 279-281, March 2025.
Anomalous left main coronary artery (LMCA) with an intraconal course is a relatively rare form of anomalous coronary artery. Intraconal LMCA typically originates from the right sinus of Valsalva. However, this report describes the very unusual …
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Milky White Supernatant in the Cardiopulmonary Bypass Circuit in Severe Hypertriglyceridemia During Pediatric Cardiac Surgery: A Case Report
Published: January 03, 2025.
Volume 16, Number 2
Pages 281-283
Contributors
Reddy Sandhya Poornima, Unnikrishnan KP, Aspari Mahammad Azeez
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 281-283, March 2025.
We present a case of severe hypertriglyceridemia (HTG) in a 21-month old female undergoing cardiac surgery for a ventricular septal defect and subaortic membrane excision. During the operation, a milky white supernatant was observed in the cardiopulmonary …
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Novel Use of the Right Atrial Appendage as a Neopulmonary Valve in a Child With Infective Endocarditis
Published: December 09, 2024.
Volume 16, Number 2
Pages 287-288
Contributors
Bharat Siddharth, Pavan Kumar Dammalapati, Vasudev V, Sameh Said
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 287-288, March 2025.
Infective endocarditis (IE) is a serious complication following any cardiac surgery.Pseudomonasas the causative organism is very rare. The authors report a case of IE post cardiac surgery for ventricular septal defect closure which was found to be …
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Three-Dimensional Imaging Defines Straddling Mitral Valve Anatomy to Allow Successful Biventricular Repair
Published: November 22, 2024.
Volume 16, Number 2
Pages 283-286
Contributors
Pezad Doctor, Irtiza S Islam, Catherine M Ikemba, Munes Fares, Jay Moore, Gregory Sturgeon, Robert DB Jaquiss, Nicholas D Andersen
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 283-286, March 2025.
Biventricular repair of a straddling mitral valve (MV) can involve relocating ectopic papillary muscles and chordae. However, this increases operative complexity and risks MV incompetence. We describe a nine-month-old with D-transposition of the great …
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The Anatomy and Embryology of Tetralogy of Fallot With Pulmonary Atresia
Published: September 06, 2024.
Volume 16, Number 2
Pages 177-182
Contributors
Vera D. Aiello1Laboratory of Pathology, Heart Institute (InCor), University of Sao Paulo School of Medicine, São Paulo, Brazil
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 177-182, March 2025.
In this review, we approach the main morphologic and developmental aspects of the congenital cardiovascular malformation known as tetralogy of Fallot with pulmonary atresia. It is recognized that pulmonary atresia associated with a deficient ventricular …
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Staged Approach: The Role of Delayed Repair Following Complete Unifocalization of Major Aortopulmonary Collateral Arteries with Ventricular Septal Defect and Pulmonary Atresia
Published: January 13, 2025.
Volume 16, Number 2
Pages 208-217
Contributors
Mimi X. Deng, Yasmin Zahiri, Osami Honjo, David J. Barron
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 208-217, March 2025.
The presentation of pulmonary vasculature in pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries (PA/VSD/MAPCA) is highly variable—as is the number, size and position of the MAPCAs and their relationship with the …
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Reader Comment on: Surgical Closure of Multiple Muscular Ventricular Septal Defects in Children Using 3D-Printed Models
Published: January 28, 2025.
Volume 16, Number 2
Pages 289-289
Contributors
Hinpetch Daungsupawong, Viroj Wiwanitkit
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 289-289, March 2025.
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Introduction to Proceedings of the World University for Pediatric and Congenital Heart Surgery Webinars About Pulmonary Atresia and Ventricular Septal Defect
Published: February 05, 2025.
Volume 16, Number 2
Pages 171-172
Contributors
Jeffrey P. Jacobs, James D. St. Louis, Darshan Reddy, Attilio A. Lotto, Osami Honjo, Sivakumar Sivalingam, Robert D. B. Jaquiss, Ignacio Juaneda, Kirsten Finucane, James K. Kirklin, Christo I. Tchervenkov, Carl L. Backer
World Journal for Pediatric and Congenital Heart Surgery, Volume 16, Issue 2, Page 171-172, March 2025.
